Malignant peripheral nerve sheath tumor (MPNST) of the nasal cavity-A rare presentation

• Author Details:   
• Gowthami Nagendhran ^*
• Mohd. Rafey
• SH Arif
• Mahboob Hasan
• Syed Iqra Usman

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Malignant peripheral nerve sheath tumors are malignant tumors arising from or differentiating from the peripheral nerve sheath cells. These tumors are more common in the upper extremities and trunk. MPNSTs arising in the head and neck region are rare, among which the nasal cavity and paranasal sinuses are the rarest locations. Diagnosing these tumors is challenging due to nonspecific clinical, radiological findings and histomorphological overlap; however, immunohistochemistry helps to distinguish them. Here, we present a case of a male patient in his 50s with a malignant peripheral nerve sheath tumor located in the nasal cavity.